Achenbach Syndrome: presentation of a case report and review of the literature
DOI:
https://doi.org/10.33448/rsd-v10i11.19672Keywords:
Achenbach Syndrome; Hematoma in the extremities; Cyanosis.Abstract
The objective of this work is to describe a case report of an adult patient whit a previous diagnosis of a autoimmune disease. Better understanding of the clinical picture and medical actions performed. The patient sought care in the city of Lages on 10/09/2019, due to a complaint of changes in hand color, beginning 4 months ago, persisting for 4 hours. No fingings of clinical significance on physical examination. During outpatient investigation, laboratory tests and arterial Doppler of the upper limbs were performed, without evidence of vasculopathy, hematological diseases or other pathologies. After excluding other diseases, Achenbach’s Syndrome became the most likely one. Due to the favorable evolution of this pathology, some medications had been prescribed for the patient’s symptomatic improvement and requests for exames to reassess the condition in 6 months. Thus, it is concluded that Achenbach’s syndrome is configured as a complex pathology, since its etiology and pathophysiology are not well defined, causing difficulty in making the diagnosis of this little-known entity.
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Copyright (c) 2021 Jéssica Lie Utiamada; Pâmela Mayara da Silva Cassemiro; Rafael Cristiano Brandl; Bertha Aparecida Davet; João Pedro Pereira da Cunha
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