Sturge-Weber Syndrome: report of a clinical case

Authors

DOI:

https://doi.org/10.33448/rsd-v10i16.23327

Keywords:

Sturge-Weber syndrome; Neurocutaneous syndromes; Angiomatosis.

Abstract

Sturge-Weber syndrome is a rare congenital developmental pathology that is not hereditary. It is characterized by cerebral cortex angiomatosis, with the presence of cerebral calcifications, epilepsy, facial nevus, and ocular alterations. The present study aimed to perform a case report of Sturge-Weber Syndrome, in a patient seen at the clinic school of the Recife School of Dentistry, presenting intraoral port wine staining, face region, pinna, and cervical region, unilateral location, right side. Because it is a rare syndrome, the present case report incorporated the other cases reported in the literature, providing more knowledge of the dental class about the disease, from the aid to diagnosis to the necessary care in the dental treatment of patients with this syndrome.

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Published

08/12/2021

How to Cite

MARTORELLI, S. . B. de F.; BARBOSA, M. R.; GHENO, C. F. da S. .; SILVA, H. F. da .; ANDRADE, B. B. de; ALVES, M. C. da M.; ROCHA, R. V. de M. .; CAVALCANTI, K. R. P. . Sturge-Weber Syndrome: report of a clinical case. Research, Society and Development, [S. l.], v. 10, n. 16, p. e120101623327, 2021. DOI: 10.33448/rsd-v10i16.23327. Disponível em: https://rsdjournal.org/index.php/rsd/article/view/23327. Acesso em: 18 apr. 2024.

Issue

Vol. 10 No. 16

Section

Health Sciences

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Copyright (c) 2021 Sérgio Bartolomeu de Farias Martorelli; Marina Rosa Barbosa; Caciana Farias da Silva Gheno; Hadassa Fonsêca da Silva; Beatriz Barbosa de Andrade; Maria Clara da Mota Alves; Rafaela Véras de Morais Rocha; Kemilly Raissa Pereira Cavalcanti

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