Dental anomalies of a child with incontinentia pigmenti: Case report

Authors

DOI:

https://doi.org/10.33448/rsd-v10i9.17482

Keywords:

Child; Incontinentia Pigmenti; Tooth abnormalities.

Abstract

Incontinentia Pigmenti is a rare multi-system dominant genetic disorder caused by a mutation of the IKBKG/NEMO gene, localized on the X-chromosome, locus Xq28, characterized by dermatological, ocular, neurological, and dental alterations. This case report shows Incontinentia Pigmenti dental findings and emphasizes the importance of the dentist's knowledge about these anomalies so that the patient can be regularly monitored throughout the development of the dentition. Keywords: Child, Incontinentia Pigmenti, Tooth Abnormalities.

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Published

03/08/2021

How to Cite

REGIS , W. F. M.; NEVES , B. G. .; LIMA, R. A. .; ROCHA , F. R. .; RODRIGUES , L. K. A. . Dental anomalies of a child with incontinentia pigmenti: Case report. Research, Society and Development, [S. l.], v. 10, n. 9, p. e50310917482, 2021. DOI: 10.33448/rsd-v10i9.17482. Disponível em: https://rsdjournal.org/index.php/rsd/article/view/17482. Acesso em: 16 apr. 2024.

Issue

Vol. 10 No. 9

Section

Health Sciences

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Copyright (c) 2021 Wanessa Fernandes Matias Regis ; Beatriz Gonçalves Neves ; Ramille Araújo Lima; Francisco Ruliglésio Rocha ; Lidiany Karla Azevedo Rodrigues

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