Hamartoma hipotalâmico: Um caso raro de puberdade precoce central no sexo masculino

Autores

DOI:

https://doi.org/10.33448/rsd-v12i14.44626

Palavras-chave:

Puberdade precoce central; Harmatoma; Hipotálamo.

Resumo

Este trabalho teve por propósito, relatar um caso raro de um menino, com pouco mais de 2 anos de idade, histórico de convulsões gelásticas e sinais de puberdade precoce. O paciente, com 1 ano e 8 meses de idade, apresentou pelos pubianos, aumento do tamanho peniano, testicular e surgimento de acnes. Somado a isto, a criança manifestava crises de risos desmotivados (convulsões gelásticas) e alteração comportamental, como agressividade diariamente.  No exame de Ressonância Nuclear Magnética da hipófise observou-se uma lesão expansiva em região hipotalâmica com parcial obliteração do aspecto posterior da cisterna suprasselar e cisterna interpeduncular, compatível com hamartoma hipotalâmico. Deu-se início ao tratamento, com o análogo do GnRH e carbamazepina. O paciente aqui relatado, segue em tratamento farmacológico.

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Publicado

28/12/2023

Como Citar

ALMEIDA, A. C. B. .; HERNANDES , S. R. C. T. . Hamartoma hipotalâmico: Um caso raro de puberdade precoce central no sexo masculino . Research, Society and Development, [S. l.], v. 12, n. 14, p. e116121444626, 2023. DOI: 10.33448/rsd-v12i14.44626. Disponível em: https://rsdjournal.org/index.php/rsd/article/view/44626. Acesso em: 25 dez. 2024.

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Ciências da Saúde